Journal Published Online: 01 May 1995
Volume 40, Issue 3

Hamartomatous Malformation of the Left Ventricle Associated with Sudden Death



We describe unusual left ventricular cardiac lesions in a 17 year old boy who died suddenly during exertion. These consisted of two grossly evident regions of deficient myocardium, containing cavernous spaces which represented exaggerated inter-trabecular regions of the left ventricular cavity. Dense fibro-elastotic tissue was deposited around these spaces along with a variable admixture of mature adipose tissue, fibrous tissue and blood vessels. The etiology of these presumably congenital developmental abnormalities is obscure. The lesions most probably represent a hamartomatous malformation, which is a poorly documented pathological entity.

Author Information

Koponen, MA
Fulton County Office of the Medical Examiner, Atlanta, GA
Siegel, R
Emory University School of Medicine and Crawford Long Hospital, Atlanta, GA
Pages: 4
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Stock #: JFS13814J
ISSN: 0022-1198
DOI: 10.1520/JFS13814J