Journal Published Online: 01 March 2001
Volume 46, Issue 2

Sudden Unexpected Death in a Patient with Splenic Sequestration and Sickle Cell-β -thalassemia Syndrome

CODEN: JFSCAS

Abstract

Acute splenic sequestration crisis is a rare disorder that usually occurs in children, with sickle cell anemia, who are under the age of five years. A few cases have been described in adults with heterozygous sickle cell syndromes. Though this entity can be fatal there have been no reported cases associated with sudden death. We describe a case of sudden, unexpected death, associated with splenic sequestration, in a 29-year-old African-American man with undiagnosed sickle cell-β+-thalassemia syndrome.

Author Information

Hutchins, KD
Regional Medical Examiner Office, Edwin H. Albano Institute of Forensic Sciences, Newark, NJ
Ballas, SK
Cardeza Foundation for Hematologic Research, Jefferson Medical College, Philadelphia, PA
Phatak, D
University of Medicine and Dentistry, State of New Jersey Medical School, Newark, NJ
Natarajan, GA
Regional Medical Examiner Office, Edwin H. Albano Institute of Forensic Sciences, Newark, NJ Office of the Medical Examiner, Perth Amboy, NJ
Pages: 3
Price: $25.00
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Stock #: JFS14985J
ISSN: 0022-1198
DOI: 10.1520/JFS14985J