ISSN: 0022-1198
CODEN: JFSCA
Page Count: 4

Hamartomatous Malformation of the Left Ventricle Associated with Sudden Death
Koponen, MA
Associate Medical Examiner, Fulton County Office of the Medical Examiner, GA

Siegel, R
Emory University School of Medicine and Crawford Long Hospital, GA

(Received 12 April 1994; accepted 16 September 1994)

Abstract

We describe unusual left ventricular cardiac lesions in a 17 year old boy who died suddenly during exertion. These consisted of two grossly evident regions of deficient myocardium, containing cavernous spaces which represented exaggerated inter-trabecular regions of the left ventricular cavity. Dense fibro-elastotic tissue was deposited around these spaces along with a variable admixture of mature adipose tissue, fibrous tissue and blood vessels. The etiology of these presumably congenital developmental abnormalities is obscure. The lesions most probably represent a hamartomatous malformation, which is a poorly documented pathological entity.

Keywords:
pathology and biology, cardiac hamartomas, sudden death

Paper ID: JFS13814J
DOI: 10.1520/JFS13814J
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